Vol. 31 (6) 2010 Neuro endocrinology letters

Elevated immunoglobulin D levels in children with PFAPA syndrome.

BACKGROUND: The periodic fever, aphthous stomatitis, pharyngitis and cervical adenitis (PFAPA) syndrome appears to be more common than generally appreciated and should be differentiated from hereditary periodic fever syndromes, particularly from mevalonate kinase deficiency (MKD).

PATIENTS AND METHODS: 14 unrelat.....